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Hydrops fetalis |
|
Fetal or neonatal death
|
Hb Bart's>80%
|
|
Hb H disease |
(-- / aacs) |
Chronic hemolytic
anemia |
Hb Bart's 20-40%
|
Hb H 5-30%
(Hb CS 2-3%) |
Thalassemia
minor |
-a / -a |
Little or no anemia;
thalassemic Rbc |
Hb Bart's 2-10% | None |
Silent carrier |
aa / aacs |
No clinical or hemolytic
abnormality |
Hb Bart's 1-2%
|
None
|
Normal |
|
No clinical or hemolytic
abnormality |
Hb Bart's 0-trace% | None |